Persistent Hyperplastic Primary Vitreous(PHPV)

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Persistent Hyperplastic Primary Vitreous(PHPV)

Cleared Controversies Commonest complication after surgery for lens extraction in PHPV is Vitreous Hemorrhage. Mittendorf dot and Bergmeister papillae are separate entities from PHPV

Remnants of hyaloid vessels Bergmeister papillae	Bergmeister papillae (Common in healthy adults) tuft of tissue at the optic disc Mittendorf dot (Common in healthy adults) tag of tissue on the posterior capsule of the lens PHPV (extensive remnants)
PHPV is	Almost always unilateral Bilaterality(rare) seen with Trisomy 13(Patau syndrome) Trisomy 22 Norrie's disease Walker Warburg syndrome
MC presenting symptom	White pupillary reflex in newborn(congenital leukocoria)
Differentiating features from retinoblastoma	PHPV Microphthalmos No calcification on CT Cataract Unilaterality No family history	Retinoblastoma Normal(usually)/buphthalmos Calcification present Cataract is rare Bilateral in one fourth cases 10% cases shows family history
Visual prognosis is	Poor despite of early intervention
Musca volitans	Residues of primitive hyaloid vasculature
Commonest complication after surgery for lens extraction in PHPV is	Vitreous Hemorrhage